Ichthyosis linearis circumflexa in a child. Response to narrowband UVB therapy.
نویسندگان
چکیده
منابع مشابه
Netherton syndrome with ichthyosis linearis circumflexa and trichorrhexis invaginatum.
Netherton syndrome is a rare, autosomal recessive disorder that is characterized by congenital ichthyosis, trichorrhexis invaginata, and atopic diathesis. Ichthyosis presents at birth with erythroderma and subsequently evolves into ichthyosis linearis circumflexa; hair shaft abnormalities tend to present later. The disorder is caused by loss-of-function mutations in the SPINK5 (serine protease ...
متن کاملIchthyosis Linearis Circumflexa as the Only Clinical Manifestation of Netherton Syndrome.
Ichthyosis linearis circumflexa (ILC) presents as serpiginous and migratory erythematous patches with double-edged scales. ILC is rarely an isolated skin manifestation, but most commonly a part of Netherton syndrome (NS). NS is caused by SPINK5 mutations, which lead to absent or sometimes reduced expression of the serine protease inhibitor LEKTI. NS is characterised by congenital ichthyosiform ...
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ژورنال
عنوان ژورنال: Journal of Dermatological Case Reports
سال: 2015
ISSN: 1898-7249
DOI: 10.3315/jdcr.2015.1214